A rare etiology of persistent jaundice in type 1 autoimmune hepatitis

Budumuri Gautam V. Kumar, Purna Ch. Sethy, Rohit Gupta

Abstract


A 24-year-old male without previously known comorbidities presented with progressive jaundice and hepatomegaly. Autoimmune serology and liver biopsy revealed features of autoimmune hepatitis. A treatment by oral prednisolone and azathioprine was initiated, after which he achieved remission. However, hyperbilirubinemia persisted, with a predominantly unconjugated fraction. Hemolytic causes of unconjugated hyperbilirubinemia were ruled out, and the diagnosis of Gilbert syndrome was established.


Keywords


autoimmune hepatitis; hyperbilirubinemia; Gilbert syndrome

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References


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DOI: http://dx.doi.org/10.22551/2021.32.0803.10183

Copyright (c) 2021 Budumuri Gautam V. Kumar, Purna Ch. Sethy, Rohit Gupta

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ISSN: 2360-6975