Underlying coeliac disease in a case of cerebellar ataxia with unknown etiology

Deepak Jain, Gourab Bhaduri, Kajaree Giri, Vikas Balania, Promil Jain


Celiac disease is an immune mediated enteropathy in susceptible individuals as a response to gluten containing diets based on wheat, oat, rye and maize. It clinically presents with malabsorption syndrome along with a myriad of extraintestinal manifestations such as anemia, osteoporosis, dermatitis herpetiformis, peripheral neuropathies, ataxia and cognitive impairment. Although the prevalence of these extraintestinal features range from 1 to 15% in these patients, their presence in the absence of intestinal manifestations is very rare. Here we report the case of a middle aged female diagnosed with celiac disease with coexisting gluten sensitive ataxia in the absence of gastrointestinal symptoms.


coeliac disease; ataxia; malabsorption; gluten

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DOI: http://dx.doi.org/10.22551/2019.22.0601.10149

Copyright (c) 2019 Deepak Jain, Gourab Bhaduri, Kajaree Giri, Vikas Balania, Promil Jain

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ISSN: 2360-6975