The cardiac electrical status of a patient with a mithocondrially inherited disease - case report

Delia Nebunu, Juan Antonio Sieira Rodríguez-Moret, Rubén Casado-Arroyo


Cardiac complications, such as myocardial disease and arrhythmias, are frequent and may be severe in patients with mitochondrial disease. Mitochondrial diseases are a heterogeneous group of disorders that can affect multiple organs with varying severity. We hereby present the case of a 58-year-old man admitted in the Cardiology Department for an Electrophysiological study asked by his General practitioner in the context of a past medical history evident for a mitochondrial cytopathy and subsequent to arrhythmic symptomatology revealed as uncomfortable palpitations and to disclosure of Holter bursts of supraventricular tachycardia.


supraventricular tachycardia, electrophysiological study, ablation, Leber disease

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